Estimation of the Prevalence of Progressive Fibrosing Interstitial Lung Diseases: Systematic Literature Review and Data from a Physician Survey
Sign Up to like & getrecommendations! Published in 2020 at "Advances in Therapy"
DOI: 10.1007/s12325-020-01578-6
Abstract: Some patients with interstitial lung diseases (ILDs) other than idiopathic pulmonary fibrosis exhibit a progressive clinical phenotype. These chronic progressive fibrosing ILDs have a variety of underlying diseases, and their prevalence is currently unknown. Here… read more here.
Keywords: per 100; prevalence; 100 000; progressive fibrosing ... See more keywords
Real-life prevalence of progressive fibrosing interstitial lung diseases.
Sign Up to like & getrecommendations! Published in 2021 at "Scientific reports"
DOI: 10.1038/s41598-021-03481-8
Abstract: The concept of progressive fibrosing interstitial lung disease (PF-ILD) has recently emerged. However, real-life proportion of PF-ILDs outside IPF is still hard to evaluate. Therefore, we sought to estimate the proportion of PF-ILD in our… read more here.
Keywords: progressive fibrosing; fibrosing interstitial; interstitial lung; real life ... See more keywords
Progressive fibrosing interstitial lung diseases: current practice in diagnosis and management
Sign Up to like & getrecommendations! Published in 2019 at "Current Medical Research and Opinion"
DOI: 10.1080/03007995.2019.1647040
Abstract: Abstract Objective: Some patients with interstitial lung diseases (ILDs) other than idiopathic pulmonary fibrosis (IPF) develop a progressive fibrosing phenotype. We investigated the diagnosis and management of non-IPF ILDs using data from a survey of… read more here.
Keywords: diagnosis; non ipf; interstitial lung; lung diseases ... See more keywords
Predictive factors for progressive fibrosing interstitial lung disease in anti‐synthetase syndrome
Sign Up to like & getrecommendations! Published in 2023 at "International Journal of Rheumatic Diseases"
DOI: 10.1111/1756-185x.14664
Abstract: Interstitial lung disease (ILD) is common in anti‐synthetase syndrome (ASS). Progressive fibrosing ILD (PF‐ILD) may develop in ILD with autoimmune features. Data on PF‐ILDs in ASS as a group are scarce. This study aimed to… read more here.
Keywords: progressive fibrosing; lung disease; synthetase syndrome; interstitial lung ... See more keywords
Nintedanib in Asian patients with progressive fibrosing interstitial lung diseases: Results from the INBUILD trial
Sign Up to like & getrecommendations! Published in 2023 at "Respirology"
DOI: 10.1111/resp.14452
Abstract: In the INBUILD trial in patients with progressive fibrosing interstitial lung diseases (ILDs), nintedanib reduced the rate of decline in forced vital capacity (FVC) with an adverse event profile characterized mainly by gastrointestinal events. We… read more here.
Keywords: fibrosing interstitial; progressive fibrosing; lung diseases; inbuild trial ... See more keywords
THU0113 RHEUMATOID ARTHRITIS ASSOCIATED INTERSTITIAL LUNG DISEASE, CLINICAL CHARACTERISTICS AND PREDICTORS OF MORTALITY
Sign Up to like & getrecommendations! Published in 2019 at "Annals of the Rheumatic Diseases"
DOI: 10.1136/annrheumdis-2019-eular.7925
Abstract: Background Interstitial lung disease (ILD) is a serious extraarticular manifestation of rheumatoid arthritis (RA) associated with excess mortality. No evidence-based approach to therapy for RA-ILD exists, but ongoing studies investigate the role of antifibrotic therapies… read more here.
Keywords: predictors mortality; fibrosing ild; progressive fibrosing; clinical characteristics ... See more keywords
Responsiveness and meaningful change thresholds of the Living with Pulmonary Fibrosis (L-PF) questionnaire Dyspnoea and Cough scores in patients with progressive fibrosing interstitial lung diseases
Sign Up to like & getrecommendations! Published in 2022 at "BMJ Open Respiratory Research"
DOI: 10.1136/bmjresp-2021-001167
Abstract: Background The Living with Pulmonary Fibrosis (L-PF) questionnaire assesses symptoms and quality of life in patients with fibrosing interstitial lung diseases (ILDs). Its Dyspnoea and Cough domains, whose items’ responses are based on a 24-hour… read more here.
Keywords: change thresholds; change; progressive fibrosing; meaningful change ... See more keywords
Real-world impact of antifibrotics on prognosis in patients with progressive fibrosing interstitial lung disease
Sign Up to like & getrecommendations! Published in 2023 at "RMD Open"
DOI: 10.1136/rmdopen-2022-002667
Abstract: Objective No studies have demonstrated the real-world efficacy of antifibrotics for progressive fibrosing interstitial lung disease (PF-ILD). Therefore, we evaluated the efficacy of antifibrotics in patients with PF-ILD. Methods We retrospectively reviewed the medical records… read more here.
Keywords: non ipf; ipf; real world; progressive fibrosing ... See more keywords
Expanding the Reach of Lung Cancer Screening: Risk Models for Individuals Who Never Smoked
Sign Up to like & getrecommendations! Published in 2022 at "American Journal of Respiratory and Critical Care Medicine"
DOI: 10.1164/rccm.202208-1521ed
Abstract: e18–e47. 2. Wells AU, Brown KK, Flaherty KR, Kolb M, Thannickal VJ; IPF Consensus Working Group. What’s in a name? That which we call IPF, by any other name would act the same. Eur Respir… read more here.
Keywords: respir; fibrosing interstitial; progressive fibrosing; lung ... See more keywords
Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases
Sign Up to like & getrecommendations! Published in 2018 at "European Respiratory Review"
DOI: 10.1183/16000617.0076-2018
Abstract: Although these conditions are rare, a proportion of patients with interstitial lung diseases (ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated with worsening respiratory symptoms, lung function decline, limited response to immunomodulatory therapies,… read more here.
Keywords: clinical course; fibrosing; interstitial lung; lung diseases ... See more keywords
Beyond idiopathic pulmonary fibrosis: the world of progressive-fibrosing interstitial lung disease
Sign Up to like & getrecommendations! Published in 2018 at "European Respiratory Review"
DOI: 10.1183/16000617.0110-2018
Abstract: In this issue, the European Respiratory Review publishes a series of articles on fibrosing interstitial lung diseases (ILDs) that present with a progressive phenotype. Progressive-fibrosing ILD (PF-ILD) is a terminology recently used to describe these… read more here.
Keywords: fibrosing interstitial; idiopathic pulmonary; interstitial lung; pulmonary fibrosis ... See more keywords