Pediatric pulmonary veno‐occlusive disease associated with a novel BMPR2 variant
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.25877
Abstract: Pulmonary veno‐occlusive disease (PVOD) and idiopathic/heritable pulmonary arterial hypertension (I/HPAH) cause progressive PH on the distinct genetic impact. A 29‐month‐old boy presented with a loss of consciousness. He had severe PH refractory to pulmonary vasodilators.… read more here.
Keywords: bmpr2 variant; veno occlusive; disease; occlusive disease ... See more keywords
Computed tomographic and clinical features of pulmonary veno-occlusive disease: raising the radiologist's awareness.
Sign Up to like & getrecommendations! Published in 2019 at "Clinical radiology"
DOI: 10.1016/j.crad.2019.04.023
Abstract: Pulmonary veno-occlusive disease (PVOD) is a rare subtype of pulmonary arterial hypertension (PAH) characterised by preferential remodelling of the pulmonary venules. Differentiation from other subtypes of PAH is essential as the management can differ significantly;… read more here.
Keywords: veno occlusive; occlusive disease; tomographic clinical; computed tomographic ... See more keywords
Clinical prediction score for identifying patients with pulmonary veno-occlusive disease/pulmonary capillary hemangiomatosis.
Sign Up to like & getrecommendations! Published in 2018 at "Journal of cardiology"
DOI: 10.1016/j.jjcc.2018.02.009
Abstract: BACKGROUND Pulmonary veno-occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) are rare causes of pulmonary hypertension. Although diagnosis is based on pathological findings, an early diagnosis is crucial because of poor prognosis compared to other… read more here.
Keywords: patients pvod; veno occlusive; pvod pch; occlusive disease ... See more keywords
Efficacy and safety of long-term imatinib therapy for patients with pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis.
Sign Up to like & getrecommendations! Published in 2017 at "Respiratory medicine"
DOI: 10.1016/j.rmed.2017.08.032
Abstract: BACKGROUND Pulmonary veno-occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) are categorized as Group 1' in the clinical classification of pulmonary hypertension. No medical therapy has been proven to be effective in patients with PVOD/PCH.… read more here.
Keywords: patients pvod; veno occlusive; pvod pch; therapy ... See more keywords
[Familial pulmonary veno-occlusive disease with a composite biallelic heterozygous EIF2AK4 mutation].
Sign Up to like & getrecommendations! Published in 2020 at "Revue des maladies respiratoires"
DOI: 10.1016/j.rmr.2020.09.004
Abstract: Pulmonary veno-occlusive disease (PVOD) is a rare cause of pulmonary hypertension. Heritable and sporadic forms have been distinguished. Hypoxemia, profound reduction in the diffusion of carbon monoxide and haemodynamic confirmation of pre-capillary pulmonary hypertension are… read more here.
Keywords: pulmonary hypertension; diagnosis; disease; pulmonary veno ... See more keywords
Clinical features of canine pulmonary veno‐occlusive disease and pulmonary capillary hemangiomatosis
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Veterinary Internal Medicine"
DOI: 10.1111/jvim.15351
Abstract: Background Histologic features of pulmonary veno‐occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) have been described in dogs but without a thorough clinical description. Objectives To report the clinical features, diagnostics, treatment, and outcome of… read more here.
Keywords: pulmonary capillary; veno occlusive; pvod pch; occlusive disease ... See more keywords
Comparison of Human and Experimental Pulmonary Veno-Occlusive Disease.
Sign Up to like & getrecommendations! Published in 2020 at "American journal of respiratory cell and molecular biology"
DOI: 10.1165/rcmb.2019-0015oc
Abstract: Pulmonary veno-occlusive disease (PVOD) occurs in humans either as heritable form (hPVOD) due to biallelic inactivating mutations of EIF2AK4 (encoding GCN2), or as a sporadic form at older age (sPVOD). The chemotherapeutic agent Mitomycin C… read more here.
Keywords: veno occlusive; occlusive disease; pvod; pulmonary veno ... See more keywords
Dyspnoea and diffuse pulmonary nodules in a patient with pulmonary veno-occlusive disease: a case report and literature review
Sign Up to like & getrecommendations! Published in 2021 at "Journal of International Medical Research"
DOI: 10.1177/0300060520986689
Abstract: Pulmonary veno-occlusive disease (PVOD) is a rare type of pulmonary hypertension characterized by capillary damage or arterial pulmonary hypertension. Early lung transplantation is the only effective treatment for PVOD because of the lack of specificity… read more here.
Keywords: occlusive disease; pvod; veno occlusive; pulmonary veno ... See more keywords
Trichloroethylene increases pulmonary endothelial permeability: implication for pulmonary veno-occlusive disease
Sign Up to like & getrecommendations! Published in 2020 at "Pulmonary Circulation"
DOI: 10.1177/2045894020907884
Abstract: Trichloroethylene exposure is a major risk factor for pulmonary veno-occlusive disease. We demonstrated that trichloroethylene alters the endothelial barrier integrity, at least in part, through vascular endothelial (VE)-Cadherin internalisation, and suggested that this mechanism may… read more here.
Keywords: occlusive disease; trichloroethylene; veno occlusive; pulmonary veno ... See more keywords
Pulmonary Veno-occlusive Disease that Developed Following Hematopoietic Stem Cell Transplantation for Acute Myeloid Leukemia
Sign Up to like & getrecommendations! Published in 2022 at "Internal Medicine"
DOI: 10.2169/internalmedicine.9811-22
Abstract: We herein report a case of pulmonary veno-occlusive disease (PVOD) induced by allo-hematopoietic stem cell transplantation (HSCT) in a 48-year-old man who was diagnosed with acute myeloid leukemia. Five months after transplantation, he developed dyspnea… read more here.
Keywords: stem cell; veno occlusive; transplantation; hematopoietic stem ... See more keywords