The foregut in cystic fibrosis
Sign Up to like & getrecommendations! Published in 2024 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.27123
Abstract: The aerodigestive organs share a kindred embryologic origin that allows for a more complete explanation as to how the foregut can remain a barrier to normalcy in people with cystic fibrosis (pwCF). The structures of… read more here.
Keywords: disease; cystic fibrosis; management; pwcf ... See more keywords
The clinical impact of the Covid-19 pandemic first wave on patients with cystic fibrosis in New York
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Cystic Fibrosis"
DOI: 10.1016/j.jcf.2022.02.012
Abstract: Background : People with cystic fibrosis (pwCF) may be at risk of complications from COVID-19 but the impact of COVID-19 on pwCF remains unknown. Methods : We conducted a multicenter retrospective cohort study to assess… read more here.
Keywords: impact covid; cystic fibrosis; pandemic first; covid ... See more keywords
Pediatric population with cystic fibrosis in the centre of Portugal: Candidates for new therapies.
Sign Up to like & getrecommendations! Published in 2021 at "Jornal de pediatria"
DOI: 10.1016/j.jped.2021.05.010
Abstract: OBJECTIVES Cystic fibrosis (CF) is a severe autosomal recessive disease that results from mutations in a gene encoding the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) protein, a chloride channel. This study aims to characterize the… read more here.
Keywords: cystic fibrosis; fibrosis; pwcf; candidates new ... See more keywords
P195 Using remote access musculoskeletal consultations within a cystic fibrosis specialist physiotherapy service: a pilot
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Cystic Fibrosis"
DOI: 10.1016/s1569-1993(21)01220-0
Abstract: During COVID-19, musculoskeletal (MSK) physiotherapists were redeployed to supplement acute staffing. Virtual clinics (VC) were used by the cystic fibrosis (CF) MDT to assess and monitor patients. Objectives: To scope benefits of providing MSK physiotherapy… read more here.
Keywords: msk; pwcf; cystic fibrosis; physiotherapy ... See more keywords
Immunoproteomic Identification of Scedosporium boydii Antigens with Potential Diagnostic Interest in Cystic Fibrosis Patients
Sign Up to like & getrecommendations! Published in 2025 at "Journal of Proteome Research"
DOI: 10.1021/acs.jproteome.5c00260
Abstract: Fungal infections caused by Scedosporium/Lomentospora species are a significant threat to patients with cystic fibrosis (pwCF), ranking as the second most common filamentous fungi in their airways after Aspergillus. Current serodiagnostic methods, such as counterimmunoelectrophoresis… read more here.
Keywords: scedosporium; boydii antigens; cystic fibrosis; scedosporium boydii ... See more keywords
Cardiac structure and function in people with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2024 at "European Heart Journal"
DOI: 10.1093/eurheartj/ehae666.3034
Abstract: Cystic fibrosis (CF) is an autosomal recessive disease affecting multiple organs, however the extent of cardiac involvement in CF is yet to be determined. The remarkable therapeutic advancements with new highly effective CF transmembrane conductance… read more here.
Keywords: structure function; function; sex; cardiac structure ... See more keywords
Association between dyspnea, chest pain, nt-probnp and cardiac impairment in people with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2024 at "European Heart Journal"
DOI: 10.1093/eurheartj/ehae666.3035
Abstract: Cystic fibrosis (CF) is an autosomal recessive disease affecting multiple organs. Emerging evidence indicates an elevated risk of cardiovascular complications in people with CF (pwCF), with some studies implicating CF-related cardiomyopathy as an underlying mechanism.… read more here.
Keywords: pain; dyspnea chest; cardiac impairment; pwcf ... See more keywords
Supplemental Oxygen Alters the Airway Microbiome in Cystic Fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "mSystems"
DOI: 10.1128/msystems.00364-22
Abstract: The airway microbiome in persons with cystic fibrosis (pwCF) is correlated with lung function and disease severity. Supplemental oxygen use is common in more advanced CF, yet its role in perturbing airway microbial communities is… read more here.
Keywords: supplemental oxygen; oxygen; pwcf; airway microbiome ... See more keywords
Nontuberculous mycobacteria remodel lung microbiota in cystic fibrosis-associated respiratory infections
Sign Up to like & getrecommendations! Published in 2025 at "Microbiology Spectrum"
DOI: 10.1128/spectrum.00382-25
Abstract: ABSTRACT Nontuberculous mycobacterial (NTM) infections in people with cystic fibrosis (pwCF) can have detrimental effects on prognosis and pose significant challenges to treatment. However, there are still questions regarding the contribution and influence of NTMs… read more here.
Keywords: cftr modulator; culture; cystic fibrosis; pwcf ... See more keywords
Role of physical activity and airway clearance therapy in cystic fibrosis: moving forward in a rapidly changing landscape
Sign Up to like & getrecommendations! Published in 2022 at "Thorax"
DOI: 10.1136/thorax-2022-219429
Abstract: Cystic fibrosis (CF) is the most common lifelimiting genetic disease. The treatment landscape of CF lung disease is changing dramatically with widespread availability of CF transmembrane conductance regulator (CFTR) modulator treatments targeting the primary protein… read more here.
Keywords: physical activity; trial; activity; pwcf ... See more keywords
Expression of ACE2—a Key SARS-CoV-2 Entry Factor—Is Not Increased in the Nasal Mucosa of People with Cystic Fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "American Journal of Respiratory Cell and Molecular Biology"
DOI: 10.1165/rcmb.2021-0341le
Abstract: Mutations in CFTR (cystic fibrosis transmembrane regulator) lead indirectly to impaired innate defense of the respiratory tract, and people with cystic fibrosis (PwCF) develop a host of bacterial and fungal infections. The role of viruses… read more here.
Keywords: genes upregulated; expression; f508del; cluster ... See more keywords