The clinical impact of the Covid-19 pandemic first wave on patients with cystic fibrosis in New York
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Cystic Fibrosis"
DOI: 10.1016/j.jcf.2022.02.012
Abstract: Background : People with cystic fibrosis (pwCF) may be at risk of complications from COVID-19 but the impact of COVID-19 on pwCF remains unknown. Methods : We conducted a multicenter retrospective cohort study to assess… read more here.
Keywords: impact covid; cystic fibrosis; pandemic first; covid ... See more keywords
Pediatric population with cystic fibrosis in the centre of Portugal: Candidates for new therapies.
Sign Up to like & getrecommendations! Published in 2021 at "Jornal de pediatria"
DOI: 10.1016/j.jped.2021.05.010
Abstract: OBJECTIVES Cystic fibrosis (CF) is a severe autosomal recessive disease that results from mutations in a gene encoding the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) protein, a chloride channel. This study aims to characterize the… read more here.
Keywords: cystic fibrosis; fibrosis; pwcf; candidates new ... See more keywords
P195 Using remote access musculoskeletal consultations within a cystic fibrosis specialist physiotherapy service: a pilot
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Cystic Fibrosis"
DOI: 10.1016/s1569-1993(21)01220-0
Abstract: During COVID-19, musculoskeletal (MSK) physiotherapists were redeployed to supplement acute staffing. Virtual clinics (VC) were used by the cystic fibrosis (CF) MDT to assess and monitor patients. Objectives: To scope benefits of providing MSK physiotherapy… read more here.
Keywords: msk; pwcf; cystic fibrosis; physiotherapy ... See more keywords
Supplemental Oxygen Alters the Airway Microbiome in Cystic Fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "mSystems"
DOI: 10.1128/msystems.00364-22
Abstract: The airway microbiome in persons with cystic fibrosis (pwCF) is correlated with lung function and disease severity. Supplemental oxygen use is common in more advanced CF, yet its role in perturbing airway microbial communities is… read more here.
Keywords: supplemental oxygen; oxygen; pwcf; airway microbiome ... See more keywords
Role of physical activity and airway clearance therapy in cystic fibrosis: moving forward in a rapidly changing landscape
Sign Up to like & getrecommendations! Published in 2022 at "Thorax"
DOI: 10.1136/thorax-2022-219429
Abstract: Cystic fibrosis (CF) is the most common lifelimiting genetic disease. The treatment landscape of CF lung disease is changing dramatically with widespread availability of CF transmembrane conductance regulator (CFTR) modulator treatments targeting the primary protein… read more here.
Keywords: physical activity; trial; activity; pwcf ... See more keywords
Expression of ACE2—a Key SARS-CoV-2 Entry Factor—Is Not Increased in the Nasal Mucosa of People with Cystic Fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "American Journal of Respiratory Cell and Molecular Biology"
DOI: 10.1165/rcmb.2021-0341le
Abstract: Mutations in CFTR (cystic fibrosis transmembrane regulator) lead indirectly to impaired innate defense of the respiratory tract, and people with cystic fibrosis (PwCF) develop a host of bacterial and fungal infections. The role of viruses… read more here.
Keywords: genes upregulated; expression; f508del; cluster ... See more keywords
Increased Safety Behavior and COVID-19-Related Fear in Adults with Cystic Fibrosis during the Pandemic
Sign Up to like & getrecommendations! Published in 2022 at "Healthcare"
DOI: 10.3390/healthcare10050858
Abstract: People with cystic fibrosis (pwCF) face great challenges during the ongoing COVID-19 pandemic. Recent research found equal levels of distress in pwCF and healthy controls (HC). The current study aimed to investigate the mental health… read more here.
Keywords: related fear; covid; covid related; pwcf ... See more keywords
Elevated Levels of Toxic Bile Acids in Serum of Cystic Fibrosis Patients with CFTR Mutations Causing Pancreatic Insufficiency
Sign Up to like & getrecommendations! Published in 2022 at "International Journal of Molecular Sciences"
DOI: 10.3390/ijms232012436
Abstract: Hepatobiliary involvement is a hallmark in cystic fibrosis (CF), as the causative CF Transmembrane Conductance Regulator (CFTR) defect is expressed in the biliary tree. However, bile acid (BA) compositions in regard to pancreatic insufficiency, which… read more here.
Keywords: cftr; pancreatic insufficiency; insufficiency; pwcf ... See more keywords