Efficacy of interleukin-1 blockade in Schnitzler’s syndrome without detectable monoclonal gammopathy: a case-based review
Sign Up to like & getrecommendations! Published in 2020 at "Clinical Rheumatology"
DOI: 10.1007/s10067-020-05501-w
Abstract: Schnitzler’s syndrome (SchS) is a rare autoinflammatory disorder characterized by urticarial rash and monoclonal gammopathy which is currently regarded as IL-1 mediated disease. We present the case of a 21-year-old woman presenting with urticarial rash,… read more here.
Keywords: schnitzler syndrome; monoclonal gammopathy; gammopathy; case ... See more keywords
Can therapeutic response to IL-1 blockade confirm the diagnosis of Schnitzler syndrome?
Sign Up to like & getrecommendations! Published in 2021 at "Clinical Rheumatology"
DOI: 10.1007/s10067-020-05565-8
Abstract: To the editor I read with great interest the article by Bixio et al. [1] describing a 21-year-old female with clinically suspected Schnitzler syndrome but without detectable monoclonal gammopathy. In view of her favorable therapeutic… read more here.
Keywords: schnitzler; monoclonal gammopathy; blockade; schnitzler syndrome ... See more keywords
Peripheral T‐cell lymphoma mimicking Schnitzler syndrome
Sign Up to like & getrecommendations! Published in 2017 at "International Journal of Rheumatic Diseases"
DOI: 10.1111/1756-185x.12893
Abstract: Dear Editor, A 53-year-old woman reported to the emergency room with intermittent fever and a disseminated pruritic rash on the chest, abdomen and limbs, present for a period of 1 month. In addition, she complained… read more here.
Keywords: lymphoma mimicking; schnitzler syndrome; cell; peripheral cell ... See more keywords
An unusual presentation of immunoglobulin A gammopathy in a patient with Schnitzler's syndrome.
Sign Up to like & getrecommendations! Published in 2023 at "International journal of rheumatic diseases"
DOI: 10.1111/1756-185x.14718
Abstract: This case summarizes a 69-year-old woman who presented with a history of recurrent fevers, widespread urticarial rash and generalized myalgias for several years with an eventual diagnosis of Schnitzler's syndrome. This is a rare autoinflammatory… read more here.
Keywords: unusual presentation; schnitzler; immunoglobulin gammopathy; presentation immunoglobulin ... See more keywords
Actinic keratoses: pain severity after cryotherapy and patient tolerability of treatment
Sign Up to like & getrecommendations! Published in 2021 at "British Journal of Dermatology"
DOI: 10.1111/bjd.19869
Abstract: sis of POEMS syndrome-associated multicentric Castleman disease was not supported by the absence of peripheral neuropathy in our case. Prior to anakinra treatment, we treated the patient with tocilizumab, which only partially improved urticarial rash… read more here.
Keywords: keratoses pain; treatment; actinic keratoses; castleman disease ... See more keywords
OP0093 RETENTION RATE OF IL-1 INHIBITORS IN PATIENTS WITH SCHNITZLER’S SYNDROME
Sign Up to like & getrecommendations! Published in 2021 at "Annals of the Rheumatic Diseases"
DOI: 10.1136/annrheumdis-2021-eular.3071
Abstract: Background: Schnitzler’s syndrome is an autoinflammatory disease characterized by monoclonal gammopathy and recurrent episodes of urticaria accompanied by clinical and laboratory signs of acute inflammation. Interleukin (IL)-1 inhibitors proved to be useful in the treatment,… read more here.
Keywords: none declared; treatment; schnitzler syndrome; retention rate ... See more keywords
Schnitzler syndrome
Sign Up to like & getrecommendations! Published in 2023 at "BMJ Case Reports"
DOI: 10.1136/bcr-2022-254334
Abstract: A woman in her late 40s with a history of psoriatic arthritis presented to us with fever, migratory rash, cervical and axillary lymphadenopathy, and generalised myalgia. Her symptoms did not improve with steroids and her… read more here.
Keywords: oncology; rheumatology; syndrome; schnitzler syndrome ... See more keywords
Schnitzler’s syndrome - a novel hypothesis of a shared pathophysiologic mechanism with Waldenström’s disease
Sign Up to like & getrecommendations! Published in 2019 at "Orphanet Journal of Rare Diseases"
DOI: 10.1186/s13023-019-1117-2
Abstract: Schnitzler’s syndrome is an auto-inflammatory disorder which is characterized by two mandatory features: an urticarial rash and a monoclonal gammopathy. Although the pathophysiology of this syndrome is not yet fully understood, a role for interleukin-1… read more here.
Keywords: pathophysiologic mechanism; schnitzler syndrome; novel hypothesis; hypothesis shared ... See more keywords
Schnitzler's syndrome: A female elderly case presenting intractable non-pruritic febrile urticarial rush.
Sign Up to like & getrecommendations! Published in 2018 at "Asian Pacific journal of allergy and immunology"
DOI: 10.12932/ap-150818-0394
Abstract: Schnitzler's syndrome is an acquired autoinflammatory disease characterized by chronic urticarial rash and monoclonal gammopathy (predominantly IgM type). A 75-year-old Japanese woman complained of high fever and non-pruritic urticarial rash appearing almost every day for… read more here.
Keywords: elderly case; non pruritic; female elderly; schnitzler syndrome ... See more keywords
Schnitzler Syndrome Presenting as a Fever of Unknown Origin with Elevated Alkaline Phosphatase Levels
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DOI: 10.2169/internalmedicine.0359-22
Abstract: Schnitzler syndrome (SchS) is a rare, acquired, autoinflammatory disease that is sometimes associated with a fever of unknown origin (FUO). Elevated alkaline phosphatase (ALP) stemming from abnormal bone remodeling is a characteristic laboratory finding of… read more here.
Keywords: unknown origin; elevated alkaline; fever unknown; alkaline phosphatase ... See more keywords
Schnitzler Syndrome after COVID-19 Vaccination
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DOI: 10.2169/internalmedicine.9598-22
Abstract: An 86-year-old Japanese woman was referred for an examination of leukocytosis and diagnosed with Waldenström macroglobulinemia. She was asymptomatic and remained stable during follow-up without treatment. The day after receiving her first COVID-19 vaccination (Pfizer-BioNTech),… read more here.
Keywords: schnitzler syndrome; syndrome covid; covid vaccination; vaccination ... See more keywords