Long Term Sirolimus therapy for LAM: a real life experience
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DOI: 10.1183/1393003.congress-2017.pa1512
Abstract: Introduction: Lymphangioleiomiomatosis (LAM) is a rare, progressive cystic lung disease, mainly affecting women. Sirolimus (SR) is effective in stabilizing lung function and in reducing the size of chylous effusions, lymphangioleiomyomas, and angiomyolipomas Objectives: Aim of… read more here.
Keywords: long term; lam; treatment; term sirolimus ... See more keywords
Pneumocystis Jirovecii Pneumonia During Sirolimus Therapy for Kaposiform Hemangioendothelioma
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DOI: 10.1542/peds.2017-1044
Abstract: An infant with KHE with KMP developed PCP while on sirolimus. Pneumocystis prophylaxis should be considered for patients receiving sirolimus. Sirolimus is an effective therapy for children with kaposiform hemangioendothelioma with or without the Kasabach-Merritt… read more here.
Keywords: pneumocystis; sirolimus; kaposiform hemangioendothelioma; sirolimus therapy ... See more keywords
Sirolimus Therapy as Perioperative Treatment of Gorham-Stout Disease in the Thoracic Spine: A Case Report
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DOI: 10.2106/jbjs.cc.17.00287
Abstract: Case: Gorham-Stout disease (GSD) is a rare entity that is marked by progressive osteolysis and bone resorption. A 14-year-old boy who was being followed for scoliosis presented with a marked curve progression and kyphoscoliosis. Imaging… read more here.
Keywords: sirolimus therapy; gorham stout; stout disease; case ... See more keywords