Default Mode Network quantitative diffusion and resting‐state functional magnetic resonance imaging correlates in sporadic Creutzfeldt‐Jakob disease
Sign Up to like & getrecommendations! Published in 2022 at "Human Brain Mapping"
DOI: 10.1002/hbm.25945
Abstract: Grey matter involvement is a well‐known feature in sporadic Creutzfeldt–Jakob disease (sCJD), yet precise anatomy‐based quantification of reduced diffusivity is still not fully understood. Default Mode Network (DMN) areas have been recently demonstrated as selectively… read more here.
Keywords: disease; creutzfeldt jakob; sporadic creutzfeldt; diffusivity ... See more keywords
Prognostic value of diffusion-weighted imaging in patients with newly diagnosed sporadic Creutzfeldt-Jakob disease
Sign Up to like & getrecommendations! Published in 2021 at "European Radiology"
DOI: 10.1007/s00330-021-08363-1
Abstract: Objectives To evaluate clinico-radiologic markers that predict poor overall survival (OS) in sporadic Creutzfeldt-Jakob disease (sCJD) and to develop a prognostic model. Materials and methods Patients with newly diagnosed sCJD were included who underwent diffusion-weighted… read more here.
Keywords: risk; creutzfeldt jakob; diffusion; sporadic creutzfeldt ... See more keywords
Correlating diffusion-weighted MRI intensity with type 2 pathology in mixed MM-type sporadic Creutzfeldt-Jakob disease
Sign Up to like & getrecommendations! Published in 2020 at "Journal of the Neurological Sciences"
DOI: 10.1016/j.jns.2019.116515
Abstract: The existence of affected subjects with both abnormal prion protein (PrPSc) types has been reported, and their clinical features were somewhat similar to the dominant PrPSc type but varied in sporadic Creutzfeldt-Jakob disease (sCJD). Presently,… read more here.
Keywords: sporadic creutzfeldt; disease; intensity; pathology ... See more keywords
Atypical and early symptoms of sporadic Creutzfeldt – Jakob disease: case series and review of the literature
Sign Up to like & getrecommendations! Published in 2020 at "International Journal of Neuroscience"
DOI: 10.1080/00207454.2020.1759594
Abstract: Abstract Background Prion diseases are rapidly progressive fatal conditions caused by abnormally shaped proteins. Sporadic Creutzfeldt - Jakob disease (sCJD) is the most common human prion disorder accounting for 85–90 % of cases. Clinical manifestations… read more here.
Keywords: early symptoms; sporadic creutzfeldt; disease; jakob disease ... See more keywords
Chronological Changes in the Expression Pattern of Hippocampal Prion Proteins During Disease Progression in Sporadic Creutzfeldt-Jakob Disease MM1 Subtype.
Sign Up to like & getrecommendations! Published in 2022 at "Journal of neuropathology and experimental neurology"
DOI: 10.1093/jnen/nlac078
Abstract: The differential effects of sporadic Creutzfeldt-Jakob disease (sCJD) on the hippocampus and other neocortical areas are poorly understood. We aimed to reveal the histological patterns of cellular prion protein (PrPC) and abnormal prion protein (PrPSc)… read more here.
Keywords: prion; sporadic creutzfeldt; creutzfeldt jakob; jakob disease ... See more keywords
Sporadic Creutzfeldt–Jakob disease presenting as epilepsia partialis continua and non‐ictal nystagmus
Sign Up to like & getrecommendations! Published in 2021 at "European Journal of Neurology"
DOI: 10.1111/ene.14847
Abstract: Creutzfeldt–Jakob disease (CJD) is a rare form of rapidly progressive neurodegenerative disorder. Seizures are uncommon in the early stage of CJD, increasing diagnostic difficulty. read more here.
Keywords: jakob disease; sporadic creutzfeldt; creutzfeldt jakob;
Diagnostic accuracy of cerebrospinal fluid biomarkers for the differential diagnosis of sporadic Creutzfeldt–Jakob disease: a (network) meta‐analysis
Sign Up to like & getrecommendations! Published in 2022 at "European Journal of Neurology"
DOI: 10.1111/ene.15258
Abstract: There are no systematic reviews of cerebrospinal fluid and blood biomarkers for sporadic Creutzfeldt–Jakob disease (sCJD) in specialized care settings that compare diagnostic accuracies in a network meta‐analysis (NMA). read more here.
Keywords: meta analysis; creutzfeldt jakob; cerebrospinal fluid; sporadic creutzfeldt ... See more keywords
Sporadic Creutzfeldt–Jakob disease with glial PrPRes nuclear and perinuclear immunoreactivity
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DOI: 10.1111/neup.12505
Abstract: Proteinase K‐resistant prion protein (PrPRes) nuclear and perinuclear immunoreactivity in oligodendrocytes of the frontal cortex is found in one case of otherwise typical sporadic Creutzfeldt‐Jakob disease (sCJD) type VV2a. The PrP nature of the inclusions… read more here.
Keywords: sporadic creutzfeldt; perinuclear immunoreactivity; jakob disease; nuclear perinuclear ... See more keywords
Sporadic Creutzfeldt-Jakob disease prion infection of human cerebral organoids
Sign Up to like & getrecommendations! Published in 2019 at "Acta Neuropathologica Communications"
DOI: 10.1186/s40478-019-0742-2
Abstract: For the transmissible, neurogenerative family of prion diseases, few human models of infection exist and none represent structured neuronal tissue. Human cerebral organoids are self-organizing, three-dimensional brain tissues that can be grown from induced pluripotent… read more here.
Keywords: sporadic creutzfeldt; prion; prion infection; disease ... See more keywords
High-Depth PRNP Sequencing in Brains With Sporadic Creutzfeldt-Jakob Disease
Sign Up to like & getrecommendations! Published in 2023 at "Neurology: Genetics"
DOI: 10.1212/nxg.0000000000200054
Abstract: Background and Objectives Sporadic Creutzfeldt-Jakob disease (sCJD) has established genetic risk factors, but, in contrast to genetic and acquired CJD, the initial trigger for misfolded prion aggregation and spread is not known. In this study,… read more here.
Keywords: disease; creutzfeldt jakob; scjd; sporadic creutzfeldt ... See more keywords
A Case of sporadic Creutzfeldt-Jakob disease
Sign Up to like & getrecommendations! Published in 2023 at "Revista da Sociedade Brasileira de Medicina Tropical"
DOI: 10.1590/0037-8682-0596-2022
Abstract: A 54-year-old male patient with no concomitant disease presented to the Neurology Clinic of Atatürk University Medical Faculty Hospital with complaints of blurred vision and sleeping difficulty for one week. His neurological examination results were… read more here.
Keywords: disease; creutzfeldt jakob; sporadic creutzfeldt; patient ... See more keywords