Susac’s syndrome as an immune-related adverse event after pembrolizumab: a case report
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Neurology"
DOI: 10.1007/s00415-019-09587-4
Abstract: Immune checkpoint inhibitors are increasingly used in cancer treatment and have a significant impact on survival [1]. Pembrolizumab is a recombinant monoclonal antibody that blocks the programmed death-1 (PD-1) receptor, which is an inhibitor of… read more here.
Keywords: response; immune related; susac syndrome; case ... See more keywords
Headache in Susac’s Syndrome
Sign Up to like & getrecommendations! Published in 2021 at "Current Pain and Headache Reports"
DOI: 10.1007/s11916-021-00939-2
Abstract: Provide an overview of the current diagnosis, pathophysiology, and treatment of Susac’s syndrome (SuS), with special emphasis on summarizing what is currently known about headache as a symptom of disease activity. The most recent literature… read more here.
Keywords: treatment; susac syndrome; sus; headache susac ... See more keywords
Exquisite response to intravenous immunoglobulin in Susac syndrome during pregnancy
Sign Up to like & getrecommendations! Published in 2018 at "eNeurologicalSci"
DOI: 10.1016/j.ensci.2017.12.004
Abstract: Introduction From its initial report on two female patients in 1979 by J.O. Susac, Susac syndrome (SuS) or SICRET (small infarctions of cochlear, retinal and encephalic tissue) has persisted as an elusive entity. To date… read more here.
Keywords: intravenous immunoglobulin; pregnancy; response intravenous; susac syndrome ... See more keywords
Gastrointestinal compromise in Susac Syndrome
Sign Up to like & getrecommendations! Published in 2017 at "Journal of the Neurological Sciences"
DOI: 10.1016/j.jns.2017.06.040
Abstract: Susac Syndrome (SuS) is an immune-mediated microvascular endotheliopathy that affects capillaries and precapillary arterioles in the brain, retina and inner ear. The immunopathogenesis is not well established, but histopathologic findings have suggested a similar mechanism… read more here.
Keywords: gastrointestinal compromise; compromise susac; susac syndrome; test ... See more keywords
Characteristics of headache in relation to the manifestation of Susac syndrome.
Sign Up to like & getrecommendations! Published in 2017 at "Medicina"
DOI: 10.1016/j.medici.2018.01.003
Abstract: Susac syndrome is characterized by a clinical triad of encephalopathy, branch retinal artery occlusion, and hearing loss. Due to the absence of the whole complex of the triad in the majority of cases at disease… read more here.
Keywords: manifestation; susac syndrome; relation; migraine like ... See more keywords
Progressive sensorineural hearing loss many years preceding completion of Susac's syndrome triad: A case report.
Sign Up to like & getrecommendations! Published in 2020 at "Multiple sclerosis and related disorders"
DOI: 10.1016/j.msard.2019.101436
Abstract: Susac's syndrome (SuS) is a rare disorder with a clinical triad of encephalopathy, sensorineural hearing loss, and branch retinal artery occlusions. We report a 7-year-old girl who presented with chronic, progressive sensorineural hearing loss, who,… read more here.
Keywords: hearing loss; sensorineural hearing; loss; susac syndrome ... See more keywords
Susac Syndrome: A Case Series.
Sign Up to like & getrecommendations! Published in 2022 at "Klinische Monatsblatter fur Augenheilkunde"
DOI: 10.1055/a-1766-6243
Abstract: BACKGROUND Susac syndrome (SS) is an autoimmune disorder that involves the eyes, the brain, and the ears. It is a rare cause of recurrent branch retinal artery occlusion. The purpose of this study was to… read more here.
Keywords: case series; syndrome case; susac syndrome;
A Novel Quantitative Assessment Method of Disease Activity in Susac's Syndrome Based on Ultra-Wide Field Imaging.
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DOI: 10.1080/02713683.2021.1967402
Abstract: PURPOSE Susac's syndrome (ScS) is a rare, potentially life-threatening auto-immune disease. Ophthalmic imaging can depict characteristic branch retinal arteriolar occlusions (BRAO) and arterial wall hyperfluorescences that form one of the three diagnostic pillars of this… read more here.
Keywords: field; quantitative assessment; susac syndrome; disease ... See more keywords
Neuropathological Findings in Susac Syndrome: An Autopsy Report.
Sign Up to like & getrecommendations! Published in 2019 at "Journal of neuropathology and experimental neurology"
DOI: 10.1093/jnen/nlz031
Abstract: A 24-year-old woman developed encephalopathy, branch retinal artery occlusion, hearing loss, and had "snowball" lesions in the corpus callosum, classic findings of Susac syndrome (SuS). Despite intensive immunosuppressive therapy, she lapsed into a coma, and… read more here.
Keywords: report neuropathological; syndrome autopsy; findings susac; susac syndrome ... See more keywords
EVALUATION OF TUMOR NECROSIS FACTOR INHIBITOR THERAPY IN SUSAC SYNDROME.
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DOI: 10.1097/iae.0000000000002466
Abstract: PURPOSE To evaluate the effect of tumor necrosis factor (TNF) inhibitor therapy on ocular relapses in patients with Susac syndrome. METHODS Multicenter retrospective cohort study of patients diagnosed with Susac syndrome according to classical clinical… read more here.
Keywords: therapy; tumor necrosis; anti tnf; susac syndrome ... See more keywords
Neuro-ophthalmic manifestations of Susac syndrome.
Sign Up to like & getrecommendations! Published in 2020 at "Current Opinion in Ophthalmology"
DOI: 10.1097/icu.0000000000000713
Abstract: PURPOSE OF REVIEW This review discusses general features and organ-specific presentations of Susac syndrome as well as diagnosis and treatment. RECENT FINDINGS Latest literature regarding demographics, new diagnostic modalities such as optical coherence tomography and… read more here.
Keywords: neuro ophthalmic; review; ophthalmology; ophthalmic manifestations ... See more keywords