Idiopathic systemic capillary leak syndrome (Clarkson syndrome) in childhood: systematic literature review
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DOI: 10.1007/s00431-018-3189-8
Abstract: Approximately 500 cases of idiopathic systemic capillary leak syndrome (Clarkson syndrome) have been reported worldwide. This life-threatening condition is characterized by episodes of increase in vascular permeability with loss of fluid into the interstitium and… read more here.
Keywords: monoclonal gammopathy; clarkson; idiopathic systemic; capillary leak ... See more keywords
Successful Treatment of a Patient with Chronic Systemic Capillary Leak Syndrome, Neutropenia and Thymoma
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DOI: 10.1007/s10875-019-00722-4
Abstract: To the Editor: Systemic capillary leak syndrome (SCLS) is a rare and potentially fatal disorder characterized by episodes of hypotension, hypoalbuminemia, and hemoconcentration as a result of increased vascular permeability [1, 2]. A rarer chronic… read more here.
Keywords: treatment; leak syndrome; capillary leak; neutropenia thymoma ... See more keywords
Handling shock in idiopathic systemic capillary leak syndrome (Clarkson’s disease): less is more
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DOI: 10.1007/s11739-019-02113-4
Abstract: Idiopathic systemic capillary leak syndrome (ISCLS) presents with recurrent potentially life-threatening episodes of hypovolemic shock associated with severe hemoconcentration and hypoproteinemia. Timely recognition is of paramount importance because ISCLS, despite resembling other kinds of hypovolemic… read more here.
Keywords: leak syndrome; idiopathic systemic; capillary leak; systemic capillary ... See more keywords
GW29-e1912 Challenges in early diagnosis of refractory shock due to systemic capillary leak syndrome:a case report and review of the literatures
Sign Up to like & getrecommendations! Published in 2018 at "Journal of the American College of Cardiology"
DOI: 10.1016/j.jacc.2018.08.857
Abstract: Systemic capillary leak syndrome (SCLS), also known as Clarkson’s disease, is a rare cause of distributive shock. The diagnosis of SCLS is often delayed and misdiagnosed. To report the refractory shock due to a SCLS… read more here.
Keywords: shock due; leak syndrome; capillary leak; refractory shock ... See more keywords
Sjögren’s syndrome concurrent with organizing pneumonia with secondary systemic capillary leak syndrome: a case report
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DOI: 10.1080/03009742.2020.1774648
Abstract: Systemic capillary leak syndrome (SCLS) is a rare, potentially fatal disease characterized by the leakage of plasma and proteins through the vascular endothelium, leading to hypotension, hypoprotei... read more here.
Keywords: gren syndrome; syndrome concurrent; leak syndrome; capillary leak ... See more keywords
Microangiopathic hemolytic anemia due to ADAMTS‐13 loss in idiopathic systemic capillary leak syndrome: comment
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DOI: 10.1111/jth.13635
Abstract: Moreira et al. describe a fascinating case of a 5-year-old who developed microangiopathic hemolytic anemia (MAHA) a week after presentation with idiopathic systemic capillary leak syndrome (SCLS) and propose ADAMTS-13 loss in the third-space fluid… read more here.
Keywords: adamts loss; leak syndrome; capillary leak; leak ... See more keywords
Systemic capillary leak syndrome (SCLS) after receiving BNT162b2 mRNA COVID-19 (Pfizer-BioNTech) vaccine
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DOI: 10.1136/bcr-2022-248927
Abstract: Systemic capillary leak syndrome (SCLS), also known as Clarkson’s disease, is a rare disorder of unknown aetiology. Since SCLS was first described in 1960, fewer than 500 cases have been reported. SCLS is diagnosed by… read more here.
Keywords: scls; systemic capillary; covid; leak syndrome ... See more keywords
A case of chronic systemic capillary leak syndrome (SCLS) exacerbated during SARS-CoV2 infection.
Sign Up to like & getrecommendations! Published in 2021 at "European review for medical and pharmacological sciences"
DOI: 10.26355/eurrev_202110_26868
Abstract: Systemic capillary leak syndrome (SCLS) is a very rare and lethal disease characterized by hemoconcentration and hypoalbuminemia caused by reversible plasma extravasation. The underlying cause for SCLS remains largely unknown and acute treatment has remained… read more here.
Keywords: leak syndrome; scls; capillary leak; syndrome scls ... See more keywords
Fatal Systemic Capillary Leak Syndrome after SARS-COV-2Vaccination in Patient with Multiple Myeloma.
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DOI: 10.3201/eid2711.211723
Abstract: A young man with smoldering multiple myeloma died of hypotensive shock 2.5 days after severe acute respiratory syndrome coronavirus 2 vaccination. Clinical findings suggested systemic capillary leak syndrome (SCLS); the patient had experienced a previous… read more here.
Keywords: multiple myeloma; capillary leak; systemic capillary; leak syndrome ... See more keywords
A Rare Case of Idiopathic Systemic Capillary Leak Syndrome
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DOI: 10.55729/2000-9666.1083
Abstract: Idiopathic systemic capillary leak syndrome (SCLS) is characterized by an increased capillary hyperpermeability with subsequent hemoconcentration, hypoproteinemia, and hypovolemia. Patients present with diffuse swelling, weight gain, low blood pressure, and shock. We present our case… read more here.
Keywords: idiopathic systemic; systemic capillary; leak syndrome; case idiopathic ... See more keywords