Successful Autologous Stem-Cell Transplantation Without the Use of Antithymocyte Globulin in a Patient with Refractory Systemic Juvenile Idiopathic Arthritis
Sign Up to like & getrecommendations! Published in 2022 at "Indian Journal of Pediatrics"
DOI: 10.1007/s12098-022-04150-y
Abstract: To the Editor: A 2-y-old female presents with a 2-mo his-tory of quotidian fever, rash, lymphadenopathy, and arthritis. After excluding infections and malignancies, systemic juvenile idiopathic arthritis (sJIA) was diagnosed and treated with methotrexate and… read more here.
Keywords: autologous stem; arthritis; systemic juvenile; stem ... See more keywords
Systemic Juvenile Idiopathic Arthritis.
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DOI: 10.1016/j.pcl.2018.04.005
Abstract: Systemic juvenile idiopathic arthritis (sJIA) is a distinctive subtype of juvenile idiopathic arthritis, characterized by fever and arthritis, often accompanied by rash, sometimes by generalized lymphadenopathy, hepatosplenomegaly, and serositis. The diagnosis requires adequate exclusion of… read more here.
Keywords: juvenile idiopathic; systemic juvenile; idiopathic arthritis;
Extracellular Vesicles in Systemic Juvenile Idiopathic Arthritis.
Sign Up to like & getrecommendations! Published in 2023 at "Journal of leukocyte biology"
DOI: 10.1093/jleuko/qiad059
Abstract: OBJECTIVES Systemic juvenile idiopathic arthritis (sJIA) is a chronic pediatric inflammatory disease of unknown etiology, characterized by fever, rash, hepatosplenomegaly, serositis and arthritis. We hypothesized that intercellular communication, mediated by extracellular vesicles (EVs), contributes to… read more here.
Keywords: extracellular vesicles; disease; arthritis; systemic juvenile ... See more keywords
Long-term Efficacy and Safety of Canakinumab in the Treatment of Systemic Juvenile Idiopathic Arthritis in Japanese Patients: Results from an Open-label Phase III Study.
Sign Up to like & getrecommendations! Published in 2022 at "Modern rheumatology"
DOI: 10.1093/mr/roac128
Abstract: OBJECTIVES To report the efficacy and safety of canakinumab treatment in Japanese patients with systemic juvenile idiopathic arthritis over a 48-week study period. METHODS Patients were administered canakinumab 4 mg/kg (maximum dose 300 mg) every 4 weeks,… read more here.
Keywords: rheumatology; canakinumab treatment; systemic juvenile; study ... See more keywords
IL-18 as a biomarker linking systemic juvenile idiopathic arthritis and macrophage activation syndrome.
Sign Up to like & getrecommendations! Published in 2019 at "Rheumatology"
DOI: 10.1093/rheumatology/kez282
Abstract: OBJECTIVES Systemic juvenile idiopathic arthritis (sJIA) is a childhood arthritis with features of autoinflammation and high risk of macrophage activation syndrome (MAS). IL-18 has been shown to have key roles in sJIA and MAS. We… read more here.
Keywords: disease; history; history mas; arthritis ... See more keywords
Role of FDG PET/CT in the Evaluation of Therapy Response in Systemic Juvenile Xanthogranuloma.
Sign Up to like & getrecommendations! Published in 2022 at "Clinical nuclear medicine"
DOI: 10.1097/rlu.0000000000004085
Abstract: ABSTRACT Juvenile xanthogranuloma, a rare type of non-Langerhans cell histiocytosis, is mostly seen in childhood and adolescence and generally manifests as widespread skin lesions. It rarely shows systemic involvement. Although the cutaneous form is often… read more here.
Keywords: therapy; fdg pet; systemic juvenile; juvenile ... See more keywords
Prognosis, complications and treatment response in systemic juvenile idiopathic arthritis patients: A single‐center experience
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DOI: 10.1111/1756-185x.13649
Abstract: Systemic juvenile idiopathic arthritis (sJIA) is a distinctive subtype of JIA characterized by systemic features and poor outcome. We aimed to investigate demographic and clinical features, long‐term treatment response and disease complications in a large… read more here.
Keywords: systemic juvenile; juvenile idiopathic; treatment response; idiopathic arthritis ... See more keywords
Factors and glucocorticoid usage affecting the prognosis of systemic juvenile idiopathic arthritis
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DOI: 10.1111/ped.14706
Abstract: The rate of glucocorticoid (GC) use is significantly higher in systemic juvenile idiopathic arthritis (SJIA) than other juvenile idiopathic arthritis subtypes. There is no consensus on the duration and dosage of GC treatment. We aimed… read more here.
Keywords: prognosis; idiopathic arthritis; systemic juvenile; juvenile idiopathic ... See more keywords
MS score in systemic juvenile idiopathic arthritis: suitable for routine use?
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DOI: 10.1136/annrheumdis-2019-216041
Abstract: We read with great interest the article by Minoia et al 1 which reported a new scoring tool for the classification of macrophage activation syndrome (MAS), a potentially life-threatening complication requiring prompt treatment, in patients… read more here.
Keywords: juvenile idiopathic; idiopathic arthritis; mas; score ... See more keywords
Response to: ‘MS score in systemic juvenile idiopathic arthritis: suitable for routine use?’ by Chi et al
Sign Up to like & getrecommendations! Published in 2019 at "Annals of the Rheumatic Diseases"
DOI: 10.1136/annrheumdis-2019-216067
Abstract: We thank Chi et al 1 for their interest in our diagnostic score for macrophage activation syndrome (MAS) in systemic juvenile idiopathic arthritis (sJIA).2 Chi et al argue that the collection of MAS patient data… read more here.
Keywords: juvenile idiopathic; score; systemic juvenile; idiopathic arthritis ... See more keywords
FRI0560 EFFICACY AND SAFETY OF ANAKINRA IN SYSTEMIC JUVENILE IDIOPATHIC ARTHRITIS – DATA OF THE BIKER REGISTRY
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DOI: 10.1136/annrheumdis-2019-eular.2608
Abstract: Background Anakinra (ANA) is recommended for treatment of systemic juvenile idiopathic arthritis (sJIA) and has recently received EMA approval. Objectives To describe safety and effectiveness of ANA in clinical practice in sJIA patients documented in… read more here.
Keywords: none; systemic juvenile; none declared; biker ... See more keywords