Pediatric pulmonary veno‐occlusive disease associated with a novel BMPR2 variant
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.25877
Abstract: Pulmonary veno‐occlusive disease (PVOD) and idiopathic/heritable pulmonary arterial hypertension (I/HPAH) cause progressive PH on the distinct genetic impact. A 29‐month‐old boy presented with a loss of consciousness. He had severe PH refractory to pulmonary vasodilators.… read more here.
Keywords: bmpr2 variant; veno occlusive; disease; occlusive disease ... See more keywords
Shear wave elastography and dispersion imaging for hepatic veno-occlusive disease prediction after pediatric hematopoietic stem cell transplantation: a feasibility study
Sign Up to like & getrecommendations! Published in 2024 at "Pediatric Radiology"
DOI: 10.1007/s00247-024-05940-6
Abstract: Non-invasive imaging modalities are warranted for diagnosing and monitoring veno-occlusive disease because early diagnosis and treatment improve the prognosis. To evaluate the usefulness of liver shear wave elastography (SWE) and shear wave dispersion (SWD) imaging… read more here.
Keywords: disease; veno occlusive; hematopoietic stem; occlusive disease ... See more keywords
Detection of Sp110 by Flow Cytometry and Application to Screening Patients for Veno-occlusive Disease with Immunodeficiency
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Clinical Immunology"
DOI: 10.1007/s10875-017-0431-5
Abstract: Mutations in Sp110 are the underlying cause of veno-occlusive disease with immunodeficiency (VODI), a combined immunodeficiency that is difficult to treat and often fatal. Because early treatment is critically important for patients with VODI, broadly… read more here.
Keywords: immunodeficiency; disease; disease immunodeficiency; veno occlusive ... See more keywords
Validation of Functional Assessment for Liver Resection Considering Venous Occlusive Area after Extended Hepatectomy
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Gastrointestinal Surgery"
DOI: 10.1007/s11605-019-04234-9
Abstract: Background Previous studies demonstrated that liver function in a veno-occlusive region is approximately 40% of that in a non-veno-occlusive region after hepatectomy with excision of major hepatic vein. We validated the preoperative assessment of future… read more here.
Keywords: frl function; occlusive region; veno occlusive; function ... See more keywords
Computed tomographic and clinical features of pulmonary veno-occlusive disease: raising the radiologist's awareness.
Sign Up to like & getrecommendations! Published in 2019 at "Clinical radiology"
DOI: 10.1016/j.crad.2019.04.023
Abstract: Pulmonary veno-occlusive disease (PVOD) is a rare subtype of pulmonary arterial hypertension (PAH) characterised by preferential remodelling of the pulmonary venules. Differentiation from other subtypes of PAH is essential as the management can differ significantly;… read more here.
Keywords: veno occlusive; occlusive disease; tomographic clinical; computed tomographic ... See more keywords
Clinical prediction score for identifying patients with pulmonary veno-occlusive disease/pulmonary capillary hemangiomatosis.
Sign Up to like & getrecommendations! Published in 2018 at "Journal of cardiology"
DOI: 10.1016/j.jjcc.2018.02.009
Abstract: BACKGROUND Pulmonary veno-occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) are rare causes of pulmonary hypertension. Although diagnosis is based on pathological findings, an early diagnosis is crucial because of poor prognosis compared to other… read more here.
Keywords: patients pvod; veno occlusive; pvod pch; occlusive disease ... See more keywords
Efficacy and safety of long-term imatinib therapy for patients with pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis.
Sign Up to like & getrecommendations! Published in 2017 at "Respiratory medicine"
DOI: 10.1016/j.rmed.2017.08.032
Abstract: BACKGROUND Pulmonary veno-occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) are categorized as Group 1' in the clinical classification of pulmonary hypertension. No medical therapy has been proven to be effective in patients with PVOD/PCH.… read more here.
Keywords: patients pvod; veno occlusive; pvod pch; therapy ... See more keywords
The role of peritoneal drainage in veno-occlusive disease in pediatric patients post hematopoietic stem cell transplant
Sign Up to like & getrecommendations! Published in 2018 at "Bone Marrow Transplantation"
DOI: 10.1038/s41409-018-0113-9
Abstract: Severe veno-occlusive disease (VOD), or sinusoidal obstruction syndrome (SOS), is a significant cause of postHSCT morbidity and mortality. This complication typically develops predominantly in the first 21 days of HSCT, although pediatric onset may be… read more here.
Keywords: sos vod; vod; veno occlusive; occlusive disease ... See more keywords
Hepatic veno-occlusive disease with asparaginase products: a review of cases reported to the FDA adverse event reporting system and published in the literature
Sign Up to like & getrecommendations! Published in 2024 at "Pediatric Hematology and Oncology"
DOI: 10.1080/08880018.2024.2395365
Abstract: Abstract Multiple asparaginase products have been approved by the United States (US) Food and Drug Administration (FDA) for the treatment of acute lymphoblastic leukemia in pediatric and adult patients. Hepatic veno-occlusive disease (VOD) is a… read more here.
Keywords: veno occlusive; hepatic vod; asparaginase products; hepatic veno ... See more keywords
Defibrotide sodium for the treatment of hepatic veno-occlusive disease/sinusoidal obstruction syndrome
Sign Up to like & getrecommendations! Published in 2018 at "Expert Review of Clinical Pharmacology"
DOI: 10.1080/17512433.2018.1421943
Abstract: ABSTRACT Introduction: Hepatic veno-occlusive disease/sinusoidal obstruction syndrome (VOD/SOS) is an unpredictable condition associated with endothelial-cell damage due to conditioning for hematopoietic stem-cell transplantation (HSCT) or chemotherapy without HSCT. Mortality in patients with VOD/SOS and multi-organ… read more here.
Keywords: vod sos; hepatic veno; treatment; disease sinusoidal ... See more keywords
Pulmonary veno‐occlusive disease: A systematic review of risk factors, clinical presentation, diagnostic investigations, treatment outcomes and prognostic factors
Sign Up to like & getrecommendations! Published in 2024 at "Journal of Medical Imaging and Radiation Oncology"
DOI: 10.1111/1754-9485.13814
Abstract: Pulmonary veno‐occlusive disease (PVOD) is a rare cause of pulmonary hypertension. We aimed to systematically evaluate published cases of PVOD to provide an overview of their clinical presentation, management and prognosis to assist early identification… read more here.
Keywords: treatment; veno occlusive; occlusive disease; clinical presentation ... See more keywords