Elucidating arrhythmogenic right ventricular cardiomyopathy with stem cells
Sign Up to like & getrecommendations! Published in 2022 at "Birth Defects Research"
DOI: 10.1002/bdr2.2010
Abstract: Human stems cells have sparked many novel strategies for treating heart disease and for elucidating their underlying mechanisms. For example, arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited heart muscle disorder that is associated with… read more here.
Keywords: ventricular cardiomyopathy; disease; right ventricular; arrhythmogenic right ... See more keywords
Acylation‐stimulating protein and heart failure progression in arrhythmogenic right ventricular cardiomyopathy
Sign Up to like & getrecommendations! Published in 2022 at "ESC Heart Failure"
DOI: 10.1002/ehf2.14218
Abstract: Our previous studies suggested that the complement system was critical in the prognosis of arrhythmogenic right ventricular cardiomyopathy (ARVC). The acylation‐stimulating protein (ASP), generated through the alternate complement pathway, was reported to regulate lipogenesis and… read more here.
Keywords: heart failure; ventricular cardiomyopathy; stimulating protein; acylation stimulating ... See more keywords
Analysis of local ventricular repolarization using unipolar recordings in patients with arrhythmogenic right ventricular cardiomyopathy
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Interventional Cardiac Electrophysiology"
DOI: 10.1007/s10840-019-00594-z
Abstract: Purpose In arrhythmogenic right ventricular cardiomyopathy (ARVC), abnormal electroanatomic mapping (EAM) areas are proportional to extent of T-wave inversion on 12-lead ECG. We aimed to evaluate local repolarization changes and their relationship to EAM substrate… read more here.
Keywords: arvc; ventricular cardiomyopathy; using unipolar; right ventricular ... See more keywords
Pathogenic variants in plakophilin-2 gene (PKP2) are associated with better survival in arrhythmogenic right ventricular cardiomyopathy.
Sign Up to like & getrecommendations! Published in 2021 at "Journal of applied genetics"
DOI: 10.1007/s13353-021-00647-y
Abstract: Arrhythmogenic right ventricular cardiomyopathy (ARVC) is mainly caused by mutations in genes encoding desmosomal proteins. Variants in plakophilin-2 gene (PKP2) are the most common cause of the disease, associated with conventional ARVC phenotype. The study… read more here.
Keywords: arvc; ventricular cardiomyopathy; right ventricular; pkp2 ... See more keywords
Sub–mitral valve aneurysm ventricular tachycardia masquerading as arrhythmogenic right ventricular cardiomyopathy
Sign Up to like & getrecommendations! Published in 2021 at "HeartRhythm Case Reports"
DOI: 10.1016/j.hrcr.2021.05.014
Abstract: Clinical re-review of all suspected ARVC cases should always be performed, especially when more Introduction The underlying etiology of ventricular tachycardia (VT) is essential for developing proper risk stratification and treatment strategies. Assessment of an… read more here.
Keywords: ventricular tachycardia; etiology; ventricular cardiomyopathy; right ventricular ... See more keywords
Clinical characteristics and determinants of phenotype in TMEM43 Arrhythmogenic right ventricular cardiomyopathy type 5.
Sign Up to like & getrecommendations! Published in 2020 at "Heart rhythm"
DOI: 10.1016/j.hrthm.2020.01.035
Abstract: BACKGROUND Arrhythmogenic right ventricular cardiomyopathy type V (ARVC-5) is the most aggressive heterozygous form of ARVC. It is predominantly caused by a fully penetrant mutation (p.S358L) in the non-desmosomal gene TMEM43 - endemic to Newfoundland,… read more here.
Keywords: ventricular cardiomyopathy; phenotype tmem43; right ventricular; background ... See more keywords
Effect of Preload Reducing Therapy on Right Ventricular Size and Function in Patients with Arrhythmogenic Right Ventricular Cardiomyopathy.
Sign Up to like & getrecommendations! Published in 2021 at "Heart rhythm"
DOI: 10.1016/j.hrthm.2021.03.018
Abstract: BACKGROUND Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is an important cause of sudden cardiac death in young people and athletes. Thus far, no treatment has proven to slow the progression of the disease. Preload reducing agents… read more here.
Keywords: ventricular cardiomyopathy; reducing agents; right ventricular; preload ... See more keywords
Systematic review: Impact of the new task force criteria in the diagnosis of arrhythmogenic right ventricular cardiomyopathy.
Sign Up to like & getrecommendations! Published in 2017 at "International journal of cardiology"
DOI: 10.1016/j.ijcard.2017.03.069
Abstract: BACKGROUND Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited disorder of cardiac desmosomes associated with ventricular arrhythmias and sudden cardiac death. The clinical diagnosis is problematic and relies on a complex criteria composed of clinical… read more here.
Keywords: ventricular cardiomyopathy; right ventricular; force criteria; three studies ... See more keywords
Pregnancy and newborn outcomes in arrhythmogenic right ventricular cardiomyopathy/dysplasia.
Sign Up to like & getrecommendations! Published in 2018 at "International journal of cardiology"
DOI: 10.1016/j.ijcard.2017.11.067
Abstract: INTRODUCTION The prognosis of pregnancy in patients with Arrhythmogenic Right Ventricular Cardiomyopathy/dysplasia (ARVC/D) is poorly documented. The aim of this study is to assess the cardiac risks during pregnancy and the impact of ARVC/D on… read more here.
Keywords: pregnancy; ventricular cardiomyopathy; right ventricular; cardiomyopathy dysplasia ... See more keywords
Arrhythmogenic left ventricular cardiomyopathy in an adolescent patient with DSP mutation
Sign Up to like & getrecommendations! Published in 2021 at "Progress in Pediatric Cardiology"
DOI: 10.1016/j.ppedcard.2021.101405
Abstract: Abstract The current understanding of the genotype-phenotype relationship in arrhythmogenic cardiomyopathy continues to evolve. Initial studies described arrhythmogenic right ventricular cardiomyopathy as a fibrofatty replacement of cardiac myocytes in the right ventricle associated with a… read more here.
Keywords: dsp mutation; ventricular cardiomyopathy; left ventricular; arrhythmogenic left ... See more keywords
CROSSTALK BETWEEN COAGULATION AND COMPLEMENT ACTIVATION IN CARDIAC DYSFUNCTION IN ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY
Sign Up to like & getrecommendations! Published in 2020 at "Journal of the American College of Cardiology"
DOI: 10.1016/s0735-1097(20)31327-9
Abstract: The role of inflammatory or immune activity in the pathogenesis of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) has not yet been widely studied. Complement is a major component of innate immunity, we study the role of… read more here.
Keywords: complement; ventricular cardiomyopathy; arrhythmogenic right; right ventricular ... See more keywords