Successful treatment of acquired von Willebrand syndrome associated with monoclonal gammopathy
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DOI: 10.1007/s00508-022-02012-3
Abstract: Acquired von Willebrand syndrome is exceedingly rare and accounts for only 1–3% of von Willebrand disease cases. In this short report, we present our own cases of acquired von Willebrand syndrome associated with monoclonal gammopathy.… read more here.
Keywords: acquired von; monoclonal gammopathy; willebrand syndrome; von willebrand ... See more keywords
Samuel Armstrong Lane's first successful treatment of haemophilia with blood transfusion in 1840: Could this also be the first successful bypassing therapy?
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DOI: 10.1111/hae.13645
Abstract: 1. Simone JV, Cornet JA, Abildgaard CF. Acquired von Willebrand’s syn‐ drome in systemic lupus erythematosus. Blood. 1968;31(6):806‐812. 2. Federici AB, RandJH, et al. Acquired von Willebrand syn‐ drome: data from an international registry. Thromb… read more here.
Keywords: willebrand syndrome; willebrand; blood; von willebrand ... See more keywords
Acquired von Willebrand syndrome and lymphoid neoplasms: A review of malignancy management, and propositions of practical recommendations
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DOI: 10.1111/hae.14648
Abstract: Acquired von Willebrand syndrome (AWS) is a rare and potentially life‐threatening bleeding disorder. AWS is primarily associated with lymphocyte‐related disorders (AWS‐LRD), such as lymphoma and IgM monoclonal gammopathy of undetermined significance (MGUS), and plasmocyte‐related disorders… read more here.
Keywords: willebrand syndrome; von willebrand; acquired von; syndrome lymphoid ... See more keywords
Good syndrome: immunodeficiency associated with thymoma
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DOI: 10.1111/imj.13950
Abstract: acquired von Willebrand syndrome: a retrospective single-centre cohort study. J Thromb Haemost 2008; 6: 569–76. 7 Vincentelli A, Susen S, Le Tourneau T, Six I, Fabre O, Juthier F et al. Acquired von Willebrand syndrome… read more here.
Keywords: willebrand syndrome; good syndrome; von willebrand; syndrome ... See more keywords
Contact activation and acquired von Willebrand syndrome during neonatal extracorporeal circulation
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DOI: 10.1111/jth.15058
Abstract: with APS and triple positivity are also positive in aPS/PT (tetra-positive aPL)7 and that aPS/PT more than aβ2GPI is responsible for LA activity in these patients.8 Finally, if aCL and aβ2GPI antibodies are of immunoglobulin… read more here.
Keywords: willebrand syndrome; syndrome neonatal; activation acquired; von willebrand ... See more keywords
ADAMTS13 inhibition to treat acquired von Willebrand syndrome during mechanical circulatory support device implantation
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Thrombosis and Haemostasis"
DOI: 10.1111/jth.15889
Abstract: Acquired von Willebrand syndrome (aVWS) is common in patients with mechanical circulatory support (MCS) devices. In these patients, the high shear stress in the device leads to increased shear‐induced proteolysis of von Willebrand factor (VWF)… read more here.
Keywords: willebrand; mechanical circulatory; circulatory support; willebrand syndrome ... See more keywords
Perioperative diagnosis and impact of acquired von Willebrand syndrome in infants with congenital heart disease.
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DOI: 10.1182/blood.2022015699
Abstract: AVWS (acquired von Willebrand syndrome) has been reported in patients with congenital heart diseases (CHD) associated with shear stress caused by significant blood flow gradients. Its etiology and impact on intraoperative bleeding during pediatric cardiac… read more here.
Keywords: congenital heart; willebrand syndrome; von willebrand; vwf ratio ... See more keywords
[Relapse of acquired von Willebrand syndrome in a patient non-compliant with Crohn's disease].
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DOI: 10.1684/abc.2021.1692
Abstract: We report a case of acquired von Willebrand syndrome relapse in association with Crohn's disease, in a context of non-compliance in a 85-year-old woman suffering from epistaxis and melena. The acquired von Willebrand syndrome is… read more here.
Keywords: willebrand syndrome; acquired von; crohn disease; von willebrand ... See more keywords
Acquired von Willebrand syndrome is common in infants with systemic-to-pulmonary shunts: Retrospective case-series
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DOI: 10.3389/fped.2022.1040128
Abstract: Background Although acquired von Willebrand syndrome (aVWS) has been described in congenital heart disease before, anatomical features leading to aVWS with characteristic reduction or loss of high molecular weight von Willebrand multimers (HMWM) are not… read more here.
Keywords: willebrand; infants systemic; willebrand syndrome; von willebrand ... See more keywords
Impact of the Severity of Acquired von Willebrand Syndrome on the Short-Term Prognosis in Patients with Temporary Mechanical Circulatory Support
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DOI: 10.3390/medicina58020238
Abstract: Background and Objectives: Acquired von Willebrand syndrome (AVWS) develops not only in patients with durable ventricular assist devices but also in patients receiving temporary mechanical circulatory support (MCS). However, its prognostic implication remains unknown. Materials… read more here.
Keywords: willebrand; index; willebrand syndrome; von willebrand ... See more keywords